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Salem K, Moazami F. Dental reconstruction in hypohydrotic ectodermal dysplasia: case report . ijpd 2016; 11 (2) :77-82
URL: http://jiapd.ir/article-1-121-en.html
URL: http://jiapd.ir/article-1-121-en.html
Abstract: (4496 Views)
Background and aim: Ectodermaldysplasia is a hereditary disorder of ectodermthat involvesteeth, skin, and hair, nails, salivary, lacrimal and sweat glands. The most common type of diseaseishypohydrotic ectodermal dysplasia that is inherited as recessive x-linked trait.
The main clinical symptoms are dry skin, sparse thinhair, small brittle nails, hyperkeratosis of palms and soles, complete or partial missing of sweat glands, hypodontia and oligodontia.
Case report:The patient was a six years oldfemalewith hypohydrotic ectodermal dysplasia with the chief complaint of difficult eating. The clinical and radiographic examinations showed conical teeth and microdontia, hypodontia, increased overbite, and atrophic alveolar ridge. The oral rehabilitation was performed by constructing overdentures on both jaws.The oral functions including mastication, speaking and esthetics were improved to a large extent.
The main clinical symptoms are dry skin, sparse thinhair, small brittle nails, hyperkeratosis of palms and soles, complete or partial missing of sweat glands, hypodontia and oligodontia.
Case report:The patient was a six years oldfemalewith hypohydrotic ectodermal dysplasia with the chief complaint of difficult eating. The clinical and radiographic examinations showed conical teeth and microdontia, hypodontia, increased overbite, and atrophic alveolar ridge. The oral rehabilitation was performed by constructing overdentures on both jaws.The oral functions including mastication, speaking and esthetics were improved to a large extent.
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Dental reconstruction in hypohydrotic ectodermal dysplasia: case report
Katayoun Salem1, Fatemeh Moazami2*.
1. Department of Pediatric Dentistry, School of Dentistry, Islamic Azad University, Tehran Branch, Tehran .Iran
2. Postgraduate student, Dept. of Pediatric Dentistry, School of Dentistry, Islamic Azad University, Tehran Branch, Tehran .Iran
Corresponding author: Fatemeh Moazami
E mail: ft.moazami88@yahoo.ca
Abstract
Background and aim: Ectodermaldysplasia is a hereditary disorder of ectodermthat involvesteeth, skin, and hair, nails, salivary, lacrimal and sweat glands. The most common type of diseaseishypohydrotic ectodermal dysplasia that is inherited as recessive x-linked trait.
The main clinical symptoms are dry skin, sparse thinhair, small brittle nails, hyperkeratosis of palms and soles, complete or partial missing of sweat glands, hypodontia and oligodontia.
Case report:The patient was a six years oldfemalewith hypohydrotic ectodermal dysplasia with the chief complaint of difficult eating. The clinical and radiographic examinations showed conical teeth and microdontia, hypodontia, increased overbite, and atrophic alveolar ridge. The oral rehabilitation was performed by constructing overdentures on both jaws.The oral functions including mastication, speaking and esthetics were improved to a large extent.
Key words: HypohydroticEctodermal dysplasia, Oral rehabilitation, Removable denture
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Case Report
|
Dental reconstruction in hypohydrotic ectodermal dysplasia: case report
Katayoun Salem1, Fatemeh Moazami2*.
1. Department of Pediatric Dentistry, School of Dentistry, Islamic Azad University, Tehran Branch, Tehran .Iran
2. Postgraduate student, Dept. of Pediatric Dentistry, School of Dentistry, Islamic Azad University, Tehran Branch, Tehran .Iran
Corresponding author: Fatemeh Moazami
E mail: ft.moazami88@yahoo.ca
Abstract
Background and aim: Ectodermaldysplasia is a hereditary disorder of ectodermthat involvesteeth, skin, and hair, nails, salivary, lacrimal and sweat glands. The most common type of diseaseishypohydrotic ectodermal dysplasia that is inherited as recessive x-linked trait.
The main clinical symptoms are dry skin, sparse thinhair, small brittle nails, hyperkeratosis of palms and soles, complete or partial missing of sweat glands, hypodontia and oligodontia.
Case report:The patient was a six years oldfemalewith hypohydrotic ectodermal dysplasia with the chief complaint of difficult eating. The clinical and radiographic examinations showed conical teeth and microdontia, hypodontia, increased overbite, and atrophic alveolar ridge. The oral rehabilitation was performed by constructing overdentures on both jaws.The oral functions including mastication, speaking and esthetics were improved to a large extent.
Key words: HypohydroticEctodermal dysplasia, Oral rehabilitation, Removable denture
Type of Article: Research Article |
Subject:
General
Received: 2017/08/20 | Accepted: 2017/08/20 | Published: 2017/08/20
Received: 2017/08/20 | Accepted: 2017/08/20 | Published: 2017/08/20
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